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. 2022 Feb 15;14(2):927–941.

Table 5.

Three- and 5-year survival outcome in derivation, validation and whole cohorts

Ewing sarcoma risk score category Derivation cohort (n=573) Validation cohort (n=287) Whole cohort (n=860)



3-year survival 5-year survival 3-year survival 5-year survival 3-year survival 5-year survival
Overall 44±2% 38±2% 48±3% 34±4% 45±2% 37±2%
Low risk (0) 73±7% 73±7% 81±8% 81±8% 76±5% 76±5%
Intermediate risk (1-3) 53±4% 47±4% 50±5% 29±5% 52±3% 39±3%
High risk (4, 5) 21±4% 14±4% 27±6% 18±6% 23±3% 15±3%