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. 2022 Feb 24;13:802355. doi: 10.3389/fgene.2022.802355

TABLE 3.

SCD-related diagnosis.

Diagnosis Incidence rate per 10,000 person months (95% CI)
SCD-SS (total person months = 18, 328.14) SCD-SC (total person months = 5, 662.55) SCD S beta-plus thalassemia (total person months = 125.52)
Sickle cell painful event 141.86 (125.73, 160.06) 203.09 (169.48, 243.36) 159.34 (40.29, 630.08)
Severe anemia secondary to hyperhemolysis 32.74 (25.43, 42.15) 14.23 (7.07, 28.24) 0
Acute malaria 17.46 (12.35, 24.68) 12.36 (5.90, 25.92) 0
Cerebrovascular accident (CVA) 12.55 (8.34, 18.88) 3.53 (0.88, 14.12) 0
Acute chest syndrome (ACS) 7.64 (4.53, 12.90) 5.30 (1.71, 16.42) 0
Avascular necrosis (AVN) 7.09 (4.12, 12.21) 21.19 (12.04, 37.29) 0
Dactylitis 5.46 (2.94, 10.14) 3.53 (0.88, 14.12) 79.67 (11.31, 561.17)
Sepsis 3.82 (1.82, 8.01) 7.06 (2.65, 18.82) 0
Priapism 2.73 (1.14, 6.56) 1.77 (0.25, 12.54) 0
Osteomyelitis 2.18 (0.82, 5.81) 1.77 (0.25, 12.54) 0

SCD-SS, sickle cell disease SS; SCD–SC, sickle cell disease SC.