TABLE 1.
CCHD, cardiovascular, and chromosomal birth defect diagnosis codes
| ICD-9-CM | ICD-10-CM | CDC/BPA | |
|---|---|---|---|
| CCHDs | |||
| Coarctation of the aorta | 747.10 | Q25.1 | 747.10–747.19 |
| Common truncus | 745.0 | Q20.0 | 745 (excluding 745.01) |
| Double outlet right ventricle | 745.11 | Q20.1 | 745.13–745.15 |
| Ebstein anomaly | 746.2 | Q22.5 | 746.20 |
| Hypoplastic left heart syndrome | 746.7 | Q23.4 | 746.70 |
| Interrupted aortic arch) | 747.11 | Prior to January 10, 2016: Q25.2, Q25.4; post January 10, 2016: Q25.21 | 747.215–747.217, 747.285 |
| Pulmonary valve atresia | 746.01 | Q22.0 | 746.00 |
| Single ventricle | 745.3 | Q20.4 | 745.3 |
| Tetralogy of Fallot | 745.2 | Q21.3 | 745.20–745.21, 747.31 |
| Total anomalous pulmonary venous connection | 747.41 | Q26.2 | 747.42 |
| Dextro-transposition of the great arteries | 745.10 | Q20.3 | 745.10, 745.11, 745.18, 745.19 |
| Tricuspid valve atresia | 746.1 | Q22.4 | 746.100 |
|
| |||
| Other cardiovascular birth defects | |||
| Aortic valve stenosis | 746.3 | Q23.0 | 746.3 |
| Atrial septal defect | 745.5 | Q21.1 | 745.51–745.59 |
| Atrioventricular septal defect | 745.60, 745.61, 745.69 | Q21.2 | 745.60–745.69, 745.487 |
| Ventricular septal defect | 745.4 | Q21.0 | 745.40–745.49 (excluding 745.487, 745.498) |
|
| |||
| Chromosomal birth defects | |||
| Deletion 22q11.2 | 758.32 | Q93.81 | 758.37 |
| Trisomy 13 | 758.1 | Q91.4–Q91.7 | 758.10–758.19 |
| Trisomy 18 | 758.2 | Q91.0–Q91.3 | 758.20–758.29 |
| Trisomy 21 | 758 | Q90.0–Q90.9 | 758.00–758.09 |
| Turner syndrome | 758.6 | Q96.0–Q96.9 | 758.60–758.69 |
Abbreviations: CDC/BPA = Centers for Disease Control and Prevention/British Pediatric Association; CCHD = critical congenital heart defect; ICD-9-CM = International Classification of Diseases, 9th revision, Clinical Modification; ICD-10-CM = International Classification of Diseases, 10th revision, Clinical Modification.