Skip to main content
. Author manuscript; available in PMC: 2023 Apr 1.
Published in final edited form as: Am J Med Genet A. 2021 Dec 16;188(4):1056–1064. doi: 10.1002/ajmg.a.62607

Figure 1.

Figure 1.

Relationships of the Vineland-3 Adaptive Behavior Composite scores in CLN3 disease. ABC scores strongly correlate withestablished measures, VIQ (A) and UBDRS sub-domain scores (B-D) and. VIQ is a standard score; UBDRS scores are weighted. Circles: Participants with classic CLN3 phenotype. Squares: Participants with vision-only phenotype. Black line: linear regression. Shaded gray area: 95% CI. ABC: adaptive behavior composite. CGI: clinical global impression. UBDRS: Unified Batten Disease Rating Scale. VIQ: verbal intelligence quotient.