Table 1.
Characteristics of Study Participants at the DAVF Initial Visit
| Evidence of | ||
|---|---|---|
| Rod Function at | ||
| DAVF Initial Visit | ||
| DAVF Initial | ||
| Visit Characteristics | No Evidence | Evidence |
| (N = 11) | (N = 38) | |
| Gender | ||
| Female | 8 (28%) | 21 (72%) |
| Male | 3 (15%) | 17 (85%) |
| Clinical diagnosis | ||
| USH2 | 9 (32%) | 19 (68%) |
| ARRP | 2 (10%) | 19 (90%) |
| Race/ethnicity | ||
| White | 8 (18%) | 36 (82%) |
| Hispanic | 2 (67%) | 1 (33%) |
| Asian | 1 (50%) | 1 (50%) |
| Enrollment area | ||
| United States/Canada | 5 (16%) | 26 (84%) |
| Europe/UK | 6 (33%) | 12 (67%) |
| Age at visit, years | ||
| Median (IQR) | 40.5 (31.0, 45.8) | 37.2 (28.0, 48.8) |
| [Min, Max] | [26.4, 64.1] | [17.8, 69.7] |
| <40 | 5 (18%) | 23 (82%) |
| ≥40 | 6 (29%) | 15 (71%) |
| Age at onset, years | ||
| Median (IQR) | 19.0 (13.0, 24.0) | 19.5 (14.0, 37.0) |
| [Min, Max] | [12.0, 27.0] | [7.0, 56.0] |
| <16 | 3 (19%) | 13 (81%) |
| [16, 25] | 6 (35%) | 11 (65%) |
| ≥25 | 2 (13%) | 14 (88%) |
| Duration of disease, years | ||
| Median (IQR) | 17.7 (12.8, 27.9) | 13.1 (7.1, 20.3) |
| [Min, Max] | [7.0, 45.1] | [2.0, 37.4] |
| <10 | 2 (13%) | 14 (88%) |
| [10, 20] | 5 (28%) | 13 (72%) |
| ≥20 | 4 (27%) | 11 (73%) |