Table 1.
SMARCB1-deficient malignant neoplasms.
SMARCB1-Deficient Mesenchymal Malignant Tumors |
SMARCB1-Deficient Non-Mesenchymal Malignant Tumors |
---|---|
Extrarenal malignant rhabdoid tumor | Atypical teratoid rhabdoid tumor |
Epithelioid sarcoma | Cribriform neuroepithelial tumor |
Poorly differentiated chordoma | Renal medullary carcinoma |
Epithelioid MPNST 1 | SMARCB1-deficient sinonasal carcinoma |
Myoepithelial carcinoma | SMARCB1-deficient carcinoma of the GI tract |
Myxoid extraskeletal chondrosarcoma |
1 malignant peripheral nerve sheath tumor.