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. 2022 Mar 11;10(3):650. doi: 10.3390/biomedicines10030650

Table 1.

SMARCB1-deficient malignant neoplasms.

SMARCB1-Deficient Mesenchymal
Malignant Tumors
SMARCB1-Deficient Non-Mesenchymal
Malignant Tumors
Extrarenal malignant rhabdoid tumor Atypical teratoid rhabdoid tumor
Epithelioid sarcoma Cribriform neuroepithelial tumor
Poorly differentiated chordoma Renal medullary carcinoma
Epithelioid MPNST 1 SMARCB1-deficient sinonasal carcinoma
Myoepithelial carcinoma SMARCB1-deficient carcinoma of the GI tract
Myxoid extraskeletal chondrosarcoma

1 malignant peripheral nerve sheath tumor.