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. 2022 Jan 1;118(1):115–373. [Article in Portuguese] doi: 10.36660/abc.20211012

Table 5-1. – Age-standardized prevalence rates of valvular heart disease per 100 000, in 1990 and 2019, and percent change of rates, in Brazil and its Federative Units.

Cause of death and Location 1990 2019 Percent Change (95% UI)
Number (95% UI) Rate (95% UI) Number (95% UI) Rate (95% UI)
B.2.1-Rheumatic heart disease (;)
Acre 3450.4 (2590.5;4467.5) 871.3 (675.4;1091.9) 8765.8 (6801.6;11017.2) 889.9 (698.1;1114.6) 2.1(-4.3;8.5)
Alagoas 21422.5 (16168.7;27275.5) 870.4 (671.7;1095.4) 34480.6 (26684.6;43431.6) 911.8 (708.5;1147.6) 4.8(-1.4;12.1)
Amapá 2291.4 (1738.2;2949.2) 877.6 (686.6;1102) 8204.3 (6320.1;10401.1) 893.7 (695.8;1127.2) 1.8(-3.6;8.2)
Amazonas 17173.8 (12858.6;21944.2) 859.3 (662.8;1072.3) 39188.9 (30084;49139) 877.9 (681.7;1093.7) 2.2(-4.5;8.7)
Bahia 102924.7 (78855.6;131748.4) 883.1 (691.6;1106.3) 153263.4 (118427;190547.8) 923.2 (714.7;1146.6) 4.5(-1.6;10.7)
Brazil 1352613.2 (1040490.6;1695888.8) 899.6 (699.8;1119.1) 2102091.3 (1639303.8;2606302.5) 918.5 (716;1142.5) 2.1(0.2;4)
Ceará 54893.6 (41770.6;69929.9) 879.9 (684.7;1108.8) 94345.5 (73759;117854.4) 907.6 (712.2;1133.8) 3.1(-3;9.6)
Distrito Federal 14943.3 (11322.7;18780.2) 882.4 (685.5;1098.2) 29679.7 (23036.6;37007.4) 884.6 (683;1107.7) 0.3(-5.5;6)
Espírito Santo 23622.8 (18038;29882.3) 883.7 (685.2;1105.3) 37781 (29560.4;47163.4) 895.2 (696.3;1123.7) 1.3(-4.7;8)
Goiás 38342.4 (29158;48881.8) 894.2 (695;1119.9) 68040.7 (52578.2;84812.4) 911.1 (703.6;1137.2) 1.9(-3.8;9.3)
Maranhão 40195 (30705.5;51338.9) 862.1 (667.6;1078.8) 74568.2 (57721.4;93956.1) 894 (691.7;1118.2) 3.7(-2.4;11)
Mato Grosso 17655.9 (13403.8;22630.5) 866.2 (670.9;1092.4) 34380.9 (26531.8;42865.4) 881.9 (679;1099.6) 1.8(-4.1;7.9)
Mato Grosso do Sul 16461.5 (12566.8;20841.5) 900.8 (701.7;1128.6) 27971.6 (21773.1;34975) 923.4 (716.7;1154.5) 2.5(-3.6;9.2)
Minas Gerais 145136.4 (111832;182475) 893.7 (700.5;1114) 210129.5 (164841.3;261917.1) 917.3 (715.3;1146) 2.6(-3.5;8.1)
Pará 41348.9 (31068.7;52497.1) 871.9 (674.1;1090.2) 87391.4 (67117.7;110404) 890.7 (690.9;1115.6) 2.2(-3.4;8.6)
Paraíba 27841.4 (21209.4;35301.7) 888.2 (685.4;1106.3) 40854.4 (31738.7;51294) 912.9 (708.4;1149.3) 2.8(-3.3;8.8)
Paraná 81156 (62014.8;102568.9) 919.2 (710.1;1145.5) 113818.3 (88747.4;140998) 939.4 (730.5;1177.7) 2.2(-3.3;7.8)
Pernambuco 63259.3 (48155.2;80253) 886 (681.7;1107.1) 96588.1 (74881.1;120052) 913.6 (707.8;1139.5) 3.1(-2.5;10.4)
Piauí 22494.3 (16958.5;28886.4) 890.4 (687.3;1117.5) 34073.1 (26412.8;42807.5) 906.3 (700.6;1139.5) 1.8(-4.7;8.5)
Rio de Janeiro 124439.1 (95279.2;157326.7) 902.8 (694.5;1137.9) 172188.9 (135252.5;212372.6) 920.6 (712.8;1140.7) 2(-4.1;7.9)
Rio Grande do Norte 21271.9 (16243;26755.5) 895.1 (696.6;1119.8) 35469.3 (27439.4;44530.2) 910 (704;1144.4) 1.7(-4.1;8.4)
Rio Grande do Sul 89482.7 (68907.8;113899.5) 930.3 (722.5;1165.4) 111269 (87372;139471) 937.4 (724.5;1173) 0.8(-5.2;6.6)
Rondônia 9709.1 (7330.4;12319.3) 862 (671.8;1077.8) 16995.1 (13142.4;21253.2) 879.4 (681;1097.4) 2(-4;8.1)
Roraima 1816.1 (1377.7;2311.1) 854.8 (666.6;1069.7) 5547.7 (4230.2;6961.8) 878.9 (678.9;1101.6) 2.8(-3.3;8.7)
Santa Catarina 44246.8 (34096.9;55614.1) 936.1 (728;1169.1) 72819.1 (57156.6;90488.1) 942.9 (735.4;1169.9) 0.7(-5.1;6.9)
São Paulo 306459.4 (235629.4;380385.5) 917.2 (710.2;1138) 455434.6 (356653.1;565502.4) 934.7 (731.5;1171.7) 1.9(-3.4;7.7)
Sergipe 12997.3 (9939.7;16567.3) 889.4 (692.3;1115.1) 23773.4 (18367.2;29453.9) 925.7 (715.4;1147.8) 4.1(-2.9;11.1)
Tocantins 7577.3 (5704.2;9694.6) 859.4 (660.2;1078.4) 15068.9 (11720.2;18871.1) 868.5 (675.1;1087.3) 1.1(-4.9;8)
B.2.5-Non-rheumatic valvular heart disease (;)
Acre 45.9 (37.3;55) 21.8 (18.2;25.8) 237.7 (200.3;276.7) 33.6 (28.4;39) 53.9(29.2;85.5)
Alagoas 317.7 (260.6;374.9) 20.8 (17.1;24.3) 1007.7 (843.5;1167.9) 29.5 (24.7;33.9) 41.6(15.4;74.6)
Amapá 31.6 (26.1;37.8) 24.8 (20.8;29) 236.1 (197;275.5) 38.4 (32.5;44.8) 54.7(27.4;87.3)
Amazonas 247.3 (204;295.5) 24.3 (20.5;28.5) 1237.1 (1037.9;1449.9) 37.7 (31.7;43.8) 55.2(30.6;84.6)
Bahia 1717.8 (1432.8;2026.8) 23 (19.5;27.1) 4952.1 (4171.7;5747.9) 29.8 (25.1;34.6) 29.2(6.4;55.7)
Brazil 26255.7 (23385;28824.5) 25.3 (22.4;27.8) 95300.5 (82828.7;108921.1) 39 (33.9;44.6) 54.3(41.1;68.3)
Ceará 938.5 (780.3;1092.3) 21.5 (18;25) 3319.7 (2799.3;3846.7) 32.5 (27.4;37.8) 51(25;84)
Distrito Federal 277.5 (231.5;328.5) 30.8 (26.2;35.6) 3271.6 (2650.9;3935.7) 110 (89.2;132) 256.6(194.9;333.7)
Espírito Santo 421.7 (344.2;499.2) 24.1 (20.2;28.2) 1776.4 (1477;2076.8) 38.5 (32.2;44.9) 59.9(32.5;91.1)
Goiás 626.9 (524.7;740.6) 23.6 (20.1;27.7) 2652.7 (2242.2;3112.3) 35 (29.6;40.9) 47.9(23.9;78.7)
Maranhão 583.9 (482.4;690.1) 20.1 (16.8;23.5) 1807.7 (1525;2100.4) 26.1 (22;30.2) 29.9(4.9;59.3)
Mato Grosso 252.7 (209.6;298.6) 23 (19.5;26.7) 1498.6 (1253.1;1755.6) 40.7 (34.2;47.7) 77.2(48.5;112)
Mato Grosso do Sul 288.6 (237.7;341.2) 25.5 (21.3;29.8) 1356.1 (1126;1592) 43.4 (36;51) 70.2(40.9;104.5)
Minas Gerais 2731.8 (2280;3218.2) 23.9 (20.2;28) 8965.3 (7605.9;10440.9) 33.4 (28.3;38.9) 39.9(17.1;69.5)
Pará 577.7 (476.5;682.4) 22 (18.4;25.6) 2437.5 (2051.8;2854.5) 31.4 (26.6;36.5) 42.9(19.1;71.9)
Paraíba 505.8 (426.6;591) 21.8 (18.4;25.4) 1401.1 (1193;1612.9) 29.8 (25.4;34.3) 36.7(13.3;66.1)
Paraná 1569.6 (1320.1;1846.9) 26.2 (22.3;30.5) 5786.1 (4865.1;6888.9) 41.5 (34.8;49.4) 58.4(32.8;87.6)
Pernambuco 1120.9 (946.9;1304.1) 22.4 (19.1;26) 3402.5 (2879.5;3968.3) 32.3 (27.2;37.6) 44(17.7;72.8)
Piauí 333.2 (271.4;393.2) 20.7 (17.2;24.2) 1013.3 (857.1;1175.3) 26.7 (22.6;31) 29.3(6.9;57.3)
Rio de Janeiro 2932 (2439;3452.2) 26.4 (22.3;31) 8945.1 (7447;10466.6) 39.3 (32.8;46) 48.6(23.7;76.8)
Rio Grande do Norte 384.4 (318.7;451.3) 23.2 (19.4;27.1) 1382.3 (1144.1;1600.7) 35 (29;40.5) 50.8(25.6;82.7)
Rio Grande do Sul 2261.2 (1899.8;2643.1) 29.7 (25.1;34.4) 6749.2 (5633.2;7857.4) 43.5 (36.4;50.6) 46.3(23.8;72.5)
Rondônia 130 (107.2;154.2) 23.1 (19.2;26.7) 648.6 (544.5;759.1) 37.4 (31.3;43.7) 61.6(34.5;95.9)
Roraima 21.3 (17;25.7) 22.2 (18.6;25.9) 162.4 (134.6;189.9) 35.6 (29.9;41.3) 60.2(30.6;93.9)
Santa Catarina 841.9 (702.4;975.8) 26.9 (22.6;31.1) 3775.8 (3163.4;4442.1) 43.5 (36.6;51) 61.7(36.3;93.4)
São Paulo 6786.6 (5675;7889) 28.1 (23.7;32.6) 26025.6 (21778.6;30883.2) 46.2 (38.8;54.9) 64.2(38.6;94.8)
Sergipe 196.5 (162.9;230.2) 21.7 (18.1;25.3) 738.2 (628.7;864.3) 30.6 (26;35.7) 41.2(16.6;72.3)
Tocantins 112.9 (93.1;134.4) 21.3 (18;25.1) 514 (434;596.7) 33.4 (28.2;38.7) 56.3(29.1;89.9)
B.2.5.1-Non-rheumatic calcific aortic valve disease (;)
Acre 10.1 (8;12.6) 5 (4;6.2) 123.4 (98;151.9) 18.5 (14.6;22.9) 266.7(224.6;314.6)
Alagoas 56.9 (45.1;70.2) 3.8 (3.1;4.7) 444.1 (354.3;546.4) 13.4 (10.7;16.5) 249.8(212;294.5)
Amapá 9.2 (7.3;11.3) 7.6 (6;9.4) 133.4 (106.8;163.6) 23.2 (18.7;28.5) 204.1(173.5;241.7)
Amazonas 70.2 (55.6;86.4) 7.3 (5.8;9) 705.8 (562.7;866.4) 22.6 (18;28) 210.8(179.8;251.5)
Bahia 404.7 (324.5;495.1) 5.5 (4.4;6.8) 2294.2 (1832.8;2814.7) 14.1 (11.2;17.3) 154.2(129.8;184.4)
Brazil 7905.4 (6333;9659.2) 7.9 (6.3;9.6) 57152.9 (45926.6;70348.4) 23.7 (19.1;29) 201.8(177.5;231.8)
Ceará 196.4 (154.7;244.3) 4.6 (3.6;5.6) 1730 (1381.8;2137) 17.2 (13.7;21.3) 276.5(231.9;332)
Distrito Federal 108.8 (85.4;132.8) 13.2 (10.5;16.3) 2764 (2173.3;3401.8) 94.8 (75;117.1) 618.3(520.2;732.3)
Espírito Santo 111.5 (88.6;136.7) 6.6 (5.3;8.2) 1049.8 (835.9;1303.9) 23.2 (18.5;28.6) 251.4(211.7;295)
Goiás 164.1 (130.9;201.4) 6.5 (5.2;8) 1421.1 (1139.4;1754.3) 19.4 (15.6;23.8) 198.4(168;237.7)
Maranhão 95.1 (74.8;119.1) 3.3 (2.6;4.1) 695.4 (554.8;852.2) 10.3 (8.2;12.6) 209.2(176.7;247.1)
Mato Grosso 63.4 (49.8;78.4) 6.2 (4.9;7.6) 919.2 (726;1132.8) 26 (20.7;32) 321(274.6;376.5)
Mato Grosso do Sul 86.4 (68.8;106) 8.1 (6.4;10) 867.8 (687.5;1078.8) 28.3 (22.6;34.8) 249.9(214.5;294)
Minas Gerais 727.1 (568.6;898.5) 6.5 (5.1;8) 4835 (3834.5;5958.1) 18.1 (14.4;22.2) 177.8(150.7;214.2)
Pará 129.4 (102.4;159.9) 5.2 (4.1;6.3) 1199.8 (951.4;1476.5) 16.2 (12.8;20) 214.6(179.7;254.2)
Paraíba 106 (83.3;131.7) 4.5 (3.6;5.7) 669.2 (532.7;821.2) 14.3 (11.4;17.6) 215(182.9;255.2)
Paraná 500.8 (399;618.4) 8.8 (7;10.8) 3677.2 (2950.2;4581.6) 26.7 (21.5;33.1) 204.3(171.8;239.2)
Pernambuco 243.8 (191.2;302.7) 5 (3.9;6.2) 1696 (1349.5;2086.2) 16.5 (13.1;20.2) 230.5(196;271.1)
Piauí 61.4 (48.4;75.5) 3.9 (3.1;4.8) 410.2 (324.2;499.1) 10.9 (8.6;13.3) 180(152.3;219.4)
Rio de Janeiro 907.3 (714.4;1122.4) 8.5 (6.8;10.5) 5421.6 (4290.2;6733.4) 23.8 (18.9;29.4) 181(153.8;214.6)
Rio Grande do Norte 95.8 (76.2;118.1) 5.8 (4.6;7.2) 762.9 (606.7;931.8) 19.6 (15.6;24) 238.6(204.2;283.4)
Rio Grande do Sul 894.7 (716.2;1105) 12.2 (9.7;15) 4459.5 (3551.3;5500.3) 28.5 (22.9;34.9) 133.9(112.6;159.4)
Rondônia 32.2 (25.2;39.9) 6.3 (5;7.8) 369.3 (291;456.9) 22.4 (17.7;27.6) 252.9(213.9;300.7)
Roraima 5.4 (4.2;6.8) 6.1 (4.8;7.5) 88.3 (69.6;109.8) 20.8 (16.6;25.8) 242(206.2;283.6)
Santa Catarina 288.2 (232.8;354) 9.6 (7.7;11.8) 2440.1 (1939.3;3004.9) 28.6 (22.9;35) 198(167.5;231)
São Paulo 2472.7 (1981.2;3024.5) 10.6 (8.5;13) 17366.6 (13732.1;21578.8) 31.1 (24.7;38.6) 193(162;227.9)
Sergipe 39.7 (31.1;49.7) 4.5 (3.6;5.6) 346.4 (275.9;428.6) 14.9 (11.8;18.5) 232(196.5;272.4)
Tocantins 24.3 (19.1;30.2) 4.8 (3.8;6) 262.7 (209.8;323.3) 17.7 (14.1;21.7) 265.3(224.9;313.9)
B.2.5.2-Non-rheumatic degenerative mitral valve disease (;)
Acre 47.4 (43.9;50.9) 21.7 (20.2;23.3) 163.5 (151.5;176.9) 21.6 (20;23.2) -0.5(-4.7;4.2)
Alagoas 346 (320;372.4) 22.2 (20.6;23.9) 761.9 (707.8;817.9) 21.9 (20.3;23.5) -1.6(-6;2.8)
Amapá 30.3 (28;32.5) 22.2 (20.6;23.8) 147.5 (135.3;160) 21.8 (20.1;23.6) -1.8(-5.6;2.1)
Amazonas 239.6 (222.1;258.5) 22.1 (20.5;23.8) 760.6 (700.6;827) 21.6 (20;23.4) -2.4(-6.9;2.3)
Bahia 1701.1 (1585.3;1824.1) 22.3 (20.7;23.9) 3654.4 (3395.5;3938.8) 21.8 (20.2;23.4) -2.3(-6.1;1.9)
Brazil 24034.9 (22437.7;25715.6) 22.5 (21;24) 53918.2 (50205.1;57756.5) 22 (20.5;23.5) -2.3(-4;-0.4)
Ceará 979.8 (914;1051.6) 22.1 (20.6;23.7) 2248.8 (2085.5;2425.1) 21.8 (20.2;23.4) -1.6(-6.1;2.6)
Distrito Federal 224.3 (207.5;242.2) 23.1 (21.5;24.7) 731.7 (675.1;789.5) 22.5 (20.9;24.2) -2.4(-7.1;2)
Espírito Santo 409.4 (381;439.6) 22.6 (21.1;24.2) 1025 (949;1104.5) 22.2 (20.6;23.9) -1.7(-5.8;2.5)
Goiás 608.1 (564.3;652.9) 22.1 (20.5;23.7) 1678.8 (1548.4;1815.2) 21.8 (20.1;23.5) -1.3(-5.6;3)
Maranhão 641.7 (595.4;691.4) 21.7 (20.2;23.4) 1520.8 (1402.1;1649.9) 21.4 (19.8;23.2) -1.5(-6.6;2.8)
Mato Grosso 251.2 (232.1;271.5) 21.6 (20.1;23.1) 828.9 (766.4;894.9) 21.7 (20.1;23.3) 0.4(-4;4.9)
Mato Grosso do Sul 261.3 (241.6;281.7) 22.1 (20.5;23.7) 692.5 (640.2;746.3) 21.9 (20.3;23.5) -1.1(-5.7;3.5)
Minas Gerais 2629.8 (2444.6;2826.8) 22.5 (21;24.1) 5799.3 (5351.7;6249.1) 21.9 (20.3;23.6) -2.6(-7;1.7)
Pará 599.1 (557;645.2) 22 (20.4;23.5) 1752.1 (1625.8;1905.2) 21.5 (20;23.3) -1.9(-6.1;2.7)
Paraíba 519.3 (482.7;555.7) 22.2 (20.6;23.7) 1015.4 (940.1;1094.2) 21.6 (20;23.3) -2.6(-6.7;1.8)
Paraná 1395.4 (1296.6;1498.3) 22.6 (21;24.2) 3058.4 (2831.7;3304.5) 22.1 (20.5;23.9) -1.9(-6.4;2.6)
Pernambuco 1150 (1065.2;1234.1) 22.6 (20.9;24.3) 2351 (2177.2;2534.8) 22.1 (20.5;23.7) -2.5(-6.6;2.2)
Piauí 357.2 (330.8;383.5) 21.9 (20.2;23.4) 819.1 (761.2;882.8) 21.5 (20;23.2) -1.4(-6.2;3.2)
Rio de Janeiro 2586.9 (2403.3;2775) 22.9 (21.3;24.6) 4954.2 (4572.2;5335.5) 22.2 (20.5;23.9) -3.2(-7.4;1.5)
Rio Grande do Norte 376.6 (350.1;404) 22.2 (20.7;23.9) 869 (804.6;936.1) 21.7 (20.1;23.4) -2.3(-6.4;1.7)
Rio Grande do Sul 1774.1 (1650.6;1908.7) 22.8 (21.3;24.5) 3317.6 (3070.6;3580.6) 22.2 (20.5;23.9) -2.9(-7;1.2)
Rondônia 128.5 (118.7;139.3) 21.5 (20;23) 389.8 (359.5;421.6) 21.5 (19.9;23.3) 0.2(-3.9;5.1)
Roraima 21.8 (20.1;23.6) 20.9 (19.4;22.5) 104.3 (96;112.7) 21.2 (19.5;22.8) 1.5(-2.6;5.8)
Santa Catarina 740.9 (687.2;794.5) 22.7 (21.1;24.3) 1915.3 (1772.8;2077.6) 22.1 (20.5;23.9) -2.9(-6.9;1.5)
São Paulo 5691.2 (5272.3;6125.5) 22.8 (21.2;24.5) 12477.6 (11520.7;13408) 22.3 (20.6;23.9) -2.4(-6.8;2)
Sergipe 207.1 (192.7;221.7) 22.4 (20.9;23.9) 536.6 (497.6;577.2) 21.8 (20.3;23.5) -2.4(-6.4;1.9)
Tocantins 117 (108.8;126.2) 21.6 (20.2;23.3) 344.2 (318.6;371.1) 21.7 (20.1;23.4) 0.4(-4;4.5)

Source: Data derived from Global Burden of Disease Study 2019, Institute for Health Metrics and Evaluation, University of Washington. 46