| AE | Allotopic expression |
| AHSCT | Allogeneic hematopoietic stem cell transplantation |
| ALS | Amyotrophic lateral sclerosis |
| ATP | Adenosine triphosphate |
| ETC | Electron transport chain |
| HR | Homologous region |
| HSP | Hereditary spastic paraplegias |
| IMS | Intermembrane space |
| iPSCs | Induced pluripotent stem cells |
| AAV/AAV2 | Adeno-associated virus (vector) |
| NADH | Nicotinamide adenine dinucleotide dehydrogenase |
| LHON | Leber’s hereditary optic neuropathy |
| NARP | Neuropathy, ataxia, and retinitis pigmentosa |
| MELAS | Mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episodes |
| MERRF | Myoclonic epilepsy with ragged-red fibers |
| MIDD | Maternally inherited diabetes and deafness |
| MILS | Maternally inherited Leigh syndrome |
| MIM/IM | Mitochondrial inner membrane |
| MNGIE | Mitochondrial neurogastrointestinal encephalomyopathy |
| mtDNA | Mitochondrial DNA |
| MTS | Mitochondrial targeting sequence |
| OXPHOS | Oxidative phosphorylation |
| RC | Respiratory complex |
| RNS | Reactive nitrogen species |
| ROS | Reactive oxygen species |
| SCA | Spinocerebellar ataxias |
| TALENS | Transcription activator-like effector nucleases |
| TM | Transmembrane domain |
| UTR | Untranslated regions |