Table 1.
Clinical features and scores of patients.
| Sections | Patient 1 | Patient 2 |
|---|---|---|
| Muscle strength | ||
| Proximal upper limb | 0 | 0 |
| Distal upper limb | 1 | 0 |
| Proximal lower limb | 0 | 0 |
| Distal lower limb | 1 | 1 |
| Torso | 0 | 0 |
| Score* | 2 | 1 |
| *: +1 score for every one-point decrease in any muscle | ||
| Sensory nerve | ||
| Neuropathic pain | 1 | 1 |
| Cold sense | 1 | 1 |
| Sensory deficiency | 1 | 1 |
| Sensory ataxia | 1 | 1 |
| Tremor | 1 | 1 |
| Score* | 5 | 5 |
| *: +1 score for any symptoms | ||
| Cranial nerve | ||
| Respiratory deficiency | 0 | 0 |
| Other nerve involvement | 0 | 0 |
| Score* | 0 | 0 |
| *: +1 score for any symptoms | ||
| Laboratory tests | ||
| CSF protein | 1 | 1 |
| Anti-Caspr1 titer | 1 | 1 |
| Score* | 2 | 2 |
| *: +1 score if CSF protein level was higher than 3g/L or if the patient had an anti-Caspr1 antibody | ||
| NCS examinations | ||
| Prolonged DML | 1 | 1 |
| Reduced CV | 1 | 1 |
| Reduced CMAP or SNAP | 1 | 1 |
| Prolonged F wave | 1 | 1 |
| Conduction blocks | 1 | 1 |
| Temporal dispersion | 0 | 0 |
| Increased CV after steroids therapy | 1 | 1 |
| Score* | 6 | 6 |
| *: a point if the CNS examination was positive | ||
CSF, cerebrospinal fluid; CV, conduction velocity; CMAP, compound muscle action potential; SNAP, sensory nerve action potential; DML, distal motor latency; NCS, nerve conduction study.