Figure 1. Oligodendrocyte precursor cells (OPCs) require TDP-43 for survival.
(A) Schematics of CreER activation. At P90, tamoxifen was administered for five consecutive days. Tissue samples were collected 14, 30, and 60 days after the last day of tamoxifen injection. (B) Pdgfra-CreER;RCE allows labeling of oligodendrocyte lineage cells. Yellow arrowheads indicate EGFP+NG2+ OPCs whereas blue arrowheads indicate EGFP+NG2− oligodendrocytes. (C) NG2 staining shows that there is a regional progression in OPC degeneration from white matter to gray matter. The dotted line separates the corpus callosum from cortex. i, ii, and iii regions are zoomed in in D. (D) Region i shows the corpus callosum with a near complete loss of OPCs at P90 + 14. ii shows loss of OPCs in the cortex at P90 + 30. iii shows highly polarized OPCs migrating from the corpus callosum up to cortex. (E) Quantification of NG2+ OPC density in corpus callosum and cortex at 14, 30, and 60 days post injection of tamoxifen (dpi). Statistical significance was determined using one-way ANOVA with Tukey’s multiple comparisons test (n = 4, ***p value < 0.001, n.s. p value >0.05). (F) Ki-67+NG2 + proliferating OPCs increase in number at P90 + 60 in the corpus callosum of PDGFRα-TDP43 KO.