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. Author manuscript; available in PMC: 2023 Feb 1.
Published in final edited form as: Expert Rev Respir Med. 2022 Jan 31;16(2):235–245. doi: 10.1080/17476348.2022.2030710

Table 1.

Disorders classified by multidisciplinary approach as idiopathic interstitial pneumonias (IIPs) as outlined by the American Thoracic Society and European Respiratory Society in 2013*

Idiopathic pulmonary fibrosis (IPF)
Idiopathic nonspecific interstitial pneumonia (idiopathic NSIP)
Respiratory bronchiolitis-interstitial lung disease (RB-ILD)
Desquamative interstitial pneumonia (DIP)
Cryptogenic organizing pneumonia (COP)
Acute interstitial pneumonia (AIP)
Idiopathic lymphoid interstitial pneumonia (idiopathic LIP)
Idiopathic pleuroparenchymal fibroelastosis (idiopathic PPFE)
Unclassifiable idiopathic interstitial pneumonia
*

adapted from the American Thoracic Society/European Respiratory Society Statement from 2013 [5].