Table 1.
Disorders classified by multidisciplinary approach as idiopathic interstitial pneumonias (IIPs) as outlined by the American Thoracic Society and European Respiratory Society in 2013*
| Idiopathic pulmonary fibrosis (IPF) |
| Idiopathic nonspecific interstitial pneumonia (idiopathic NSIP) |
| Respiratory bronchiolitis-interstitial lung disease (RB-ILD) |
| Desquamative interstitial pneumonia (DIP) |
| Cryptogenic organizing pneumonia (COP) |
| Acute interstitial pneumonia (AIP) |
| Idiopathic lymphoid interstitial pneumonia (idiopathic LIP) |
| Idiopathic pleuroparenchymal fibroelastosis (idiopathic PPFE) |
| Unclassifiable idiopathic interstitial pneumonia |
adapted from the American Thoracic Society/European Respiratory Society Statement from 2013 [5].