Table 4.

Reported relative types in familial ILD

	All	Sarc	HP	IPF	uPF	non-IPF IIP	aidILD	oILD
Any ILD, n (%)	174	103	10	26	20	1	7	7
1st degree relative	125 (72)	64 (62)	9 (90)	23 (88)	17 (85)	1 (100)	6 (86)	5 (71)
Other relative	70 (40)	52 (50)	2 (20)	7 (27)	6 (30)	0	1 (14)	2 (29)
Only other relative	49 (28)	39 (38)	1 (10)	3 (12)	3 (15)	0	1 (14)	2 (29)
Sarcoidosis	109	90	4	3	5	0	3	4
1st degree relative	70 (64)	54 (60)	3 (75)	3 (100)	5 (100)	0	3 (100)	2 (50)
Other relative	49 (45)	46 (51)	1 (25)	0	0	0	0	2 (50)
Only other relative	39 (36)	36 (40)	1 (25)	0	0	0	0	2 (50)
Pulmonary fibrosis	54	7	5	22	15	0	4	1
1st degree relative	45 (83)	5 (71)	5 (100)	19 (86)	12 (80)	0	3 (75)	1 (100)
Other relative	15 (28)	2 (29)	1 (20)	7 (32)	4 (27)	0	1 (25)	0
Only other relative	9 (17)	2 (29)	0	3 (14)	3 (20)	0	1 (25)	0
Remaining ILD	20	11	1	2	3	1	0	2
1st degree	14 (70)	7 (64)	1 (100)	2 (100)	1 (33)	1 (100)	0	2 (100)
Other relative	7 (35)	5 (45)	0	0	2 (67)	0	0	0
Only other relative	6 (30)	4 (36)	0	0	2 (67)	0	0	0

HP = hypersensitivity pneumonitis; IPF = idiopathic pulmonary fibrosis; uPF = unclassifiable pulmonary fibrosis; non-IPF IIP = idiopathic interstitial pneumonia other than IPF; aidILD = autoimmune ILD; oILD = other ILD. Familial disease is an ILD patient reporting one or more relatives with an ILD