Figure 1.

Phenotypic features of arrhythmogenic left ventricular cardiomyopathy. ECG strips showing low QRS voltages (<0.5 mV) in the limb leads (arrow) (A), negative T-waves in leads V4–V6 (arrows) (B), premature ventricular beat with a right bundle branch block and superior axis (C), and ventricular tachycardia with a right bundle branch block and inferior axis morphology (D). Two-dimensional echocardiogram (diastolic frame in four-chamber view) showing a non-dilated and normokinetic (not shown) left ventricle (E). Cardiac magnetic resonance (diastolic frame of four-chamber view on postcontrast sequences) showing diffuse late gadolinium enhancement involving the subepicardial layer of the left ventricle free wall and the septum (F). Histological panoramic view of the posterolateral left ventricular wall showing replacement-type myocardial fibrosis mostly involving the subepicardial layer (trichrome stain) (G).