Figure 4.

Left ventricular remodelling and regional distribution of LGE in ACM-LV phenotype versus DCM-LV phenotype. Comparison between CMR findings in the subgroup of patients with ACM (left) and patients with DCM (right) with overlapping LV phenotypes (ie, LV systolic dysfunction and LV LGE) shows that (1) ACM has lower LV volume and mass, less depressed LVEF (not shown) and greater amount of LV LGE (ie, ‘hypokinetic, non‐dilated and fibrotic left ventricle’) compared with patients with DCM); (2) LV LGE predominately affects the inferolateral segments in ACM and septal segments in DCM; and (3) in ACM the LV LGE appears as a stria pattern that more frequently affects the subepicardial layers, compared with the spot/patchy pattern and the mid-myocardial location of DCM. Modified from Cipriana et al.²² ACM, arrhythmogenic cardiomyopathy; ARVC, arrhythmogenic right ventricular (dysplasia/) cardiomyopathy; CMR, cardiac magnetic resonance; DCM, dilated cardiomyopathy; LGE, late gadolinium enhancement; LV, left ventricular; LVEF, left ventricular ejection fraction.