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. 2022 Apr 1;19(4):572–582. doi: 10.1513/AnnalsATS.202105-560OC

Table 3.

Patient characteristics (Penn Cohort)

  n = 60
Age, yr 50 ± 18
Sex, female, % 100
Body mass index, kg/m2 28 ± 6.2
Race, %
 White 58
 African American 32
 Other 10
PAH etiology, %
 Idiopathic/heritable 50
 Connective tissue disease 31
 Other 19
PAH medications, %
 Only oral 56
 Inhaled ± oral 9
 Parenteral prostacyclin analog ± oral 35
WHO functional class, %
 I 9
 II 46
 III 45
emPHasis-10 19 ± 12
6-minute walk distance, m 403 ± 129
TAPSE, cm 2.0 (1.7–2.2)
Accelerometry variables (per day)
 Vector magnitude counts 1,860,000 ± 613,800
 Step counts 7,960 ± 2,710
 Sedentary, min 333 (255–396)
 Light activity, min 236 (207–260)
 Moderate activity, min 16 (12–29)

Definition of abbreviations: PAH = pulmonary arterial hypertension; Penn = Pennsylvania; TAPSE = tricuspid annular plane systolic excursion; WHO = World Health Organization.

Data are summarized as mean ± SD or median (interquartile range).