Table 3.
Patient characteristics (Penn Cohort)
n = 60 | |
---|---|
Age, yr | 50 ± 18 |
Sex, female, % | 100 |
Body mass index, kg/m2 | 28 ± 6.2 |
Race, % | |
White | 58 |
African American | 32 |
Other | 10 |
PAH etiology, % | |
Idiopathic/heritable | 50 |
Connective tissue disease | 31 |
Other | 19 |
PAH medications, % | |
Only oral | 56 |
Inhaled ± oral | 9 |
Parenteral prostacyclin analog ± oral | 35 |
WHO functional class, % | |
I | 9 |
II | 46 |
III | 45 |
emPHasis-10 | 19 ± 12 |
6-minute walk distance, m | 403 ± 129 |
TAPSE, cm | 2.0 (1.7–2.2) |
Accelerometry variables (per day) | |
Vector magnitude counts | 1,860,000 ± 613,800 |
Step counts | 7,960 ± 2,710 |
Sedentary, min | 333 (255–396) |
Light activity, min | 236 (207–260) |
Moderate activity, min | 16 (12–29) |
Definition of abbreviations: PAH = pulmonary arterial hypertension; Penn = Pennsylvania; TAPSE = tricuspid annular plane systolic excursion; WHO = World Health Organization.
Data are summarized as mean ± SD or median (interquartile range).