Table 1.
All n (%) |
Adults n (%) |
Children n (%) |
|
---|---|---|---|
Number of total patients | 46 (100.0) | 31 (100.0) | 15 (100.0) |
Type of haemophilia: | |||
A | 39 (84.8) | 26 (83.9) | 13 (86.7) |
B | 7 (15.2) | 5 (16.1) | 2 (13.3) |
Degree of haemophilia: | |||
Mild | 14 (30.4) | 14 (45.2) | |
Moderate | 4 (8.7) | 4 (12.9) | |
Severe | 28 (60.9) | 13 (41.9) | 15 (100.0) |
Family history: | |||
Family | 19 (41.3) | 14 (45.2) | 5 (33.4) |
Sporadic | 27 (58.7) | 17 (54.8) | 10 (66.6) |
Inhibitor: | |||
Yes | 5 (10.9) | 2 (6.5) | 3 (20.0) |
No | 41 (89.1) | 29 (95.5) | 12 (80.0) |
Viral Infections: | |||
None | 22 (47.8) | 7 (22.6) | 15 (100.0) |
HCV | 23 (50.0) | 23 (74.2) | |
HIV | 3 (6.5) | 3 (9.7) | |
HBV | 2 (4.3) | 2 (6.5) | |
Other | 1 (2.2) | 1 (3.2) | |
Trauma: | |||
No | 32 (69.6) | 25 (80.6) | 7 (46.7) |
Yes | 12 (26.1) | 6 (19.4) | 6 (40.0) |
Peri-Partum | 2 (4.3) | 2 (13.3) | |
Smoke: | |||
Yes | 10 (32.3) | 10 (32.3) | NA |
No | 17 (58.8) | 17 (58.8) | NA |
Not reported | 4 (12.9) | 4 (12.9) | NA |
Alcohol intake: | |||
No | 11 (35.5) | 11 (35.5) | NA |
Usually | 13 (41.9) | 13 (41.9) | NA |
Rarely | 3 (9.7) | 3 (9.7) | NA |
Not reported | 4 (12.9) | 4 (12.9 | NA |
* Symptoms at diagnosis: | |||
None | 13 (28.2) | 11 (35.5) | 2 (13.3) |
Headache | 12 (26.0) | 9 (29.0) | 3 (20.0) |
Epilepsy | 4 (8.7) | 1 (3.2) | 3 (20.0) |
Motor dysfunction | 4 (8.7) | 3 (9.7) | 1 (6.7) |
Syncope | 1 (2.2) | 1 (3.2) | |
Asthenia | 5 (10.9) | 4 (12.9) | 1 (6.7) |
Drowsiness | 7 (15.2) | 4 (12.9) | 3 (20.0) |
Coma | 7 (15.2) | 5 (16.1) | 5 (33.4) |
Vomiting | 2 (4.3) | 1 (3.2) | 1 (6.7) |
Other | 3 (6.5) | 3 (9.7) | |
* Site of ICH: | |||
Intraparenchymal | 21 (45.7) | 16 (51.6) | 5 (33.4) |
Subdural | 8 (17.4) | 4 (12.9) | 4 (26.7) |
Subarachnoid | 9 (19.6) | 6 (19.4) | 3 (20.0) |
Intraventricular | 2 (4.3) | 2 (13.3) | |
Not specified | 11 (23.9) | 8 (25.8) | 3 (20.0) |
Sequelae: | |||
All | 13 (28.2) | 8 (25.8) | 5 (33.4) |
Neurological | 5 (10.9) | 2 (6.5) | 3 (20.0) |
Recurrences | 2 (4.3) | 1 (3.2) | 1 (6.7) |
Deaths | 14 (30.4) | 13 (41.9) | 1 (6.7) |