TABLE 2.

Family history in relation to hearing loss onset and progression

Family History	Total	Early Onset	Late Onset
Autosomal-recessive	66 (22%)	38 (57%)	28 (43%)
Stable		26 (68%)	6 (21%)
Progressive		12 (32%)	22 (79%)
Autosomal-dominant	79 (26%)	21 (27%)	58 (73%)
Stable		8 (38%)	4 (7%)
Progressive		13 (62%)	54 (93%)
X-linked	2 (1%)	1 (50%)	1 (50%)
Stable		0 (0%)	0 (0%)
Progressive		1 (100%)	1 (100%)
Sporadic	158 (52%)	66 (42%)	92 (58%)
Stable		39 (59%)	19 (21%)
Progressive		27 (41%)	73 (79%)

Early hearing loss onset refers to congenital/pre/perilingual onset (≤6 years of age).

Late hearing loss onset refers to postlingual onset (>6 years of age).