Table 1.
Baseline characteristics of the study participants (n = 13)
| Characteristic | Value | |||
| Age (years), mean (SD) | 48.9 (9.9) | |||
| Gender M/F, n (%) | 9 (69.2)/4 (30.8) | |||
| Weight (kg), mean (SD) | 67.9 (13.3) | |||
| Height (cm), mean (SD) | 168.6 (8.5) | |||
| Time since symptom onset (months), median (IQR) | 13.6 (8.1, 17.8) | |||
| Time since diagnosis (months), median (IQR) | 1.9 (1.1, 14.8) | |||
| Region affected | First body part | At baseline | ||
| UMN (clinical) | LMN (clinical) | LMN (EMG) | ||
| Bulbar, n (%) | 5 (38.5) | 7 (53.8) | 7 (53.8) | 12 (92.3) |
| Left upper extremity, n (%) | 1 (7.7) | 11 (84.6) | 11 (84.6) | 13 (100) |
| Right upper extremity, n (%) | 4 (30.8) | 12 (92.3) | 11 (84.6) | 13 (100) |
| Trunk, n (%) | 0 (0) | 5 (38.5)* | 5 (38.5) | 13 (100) |
| Left lower extremity, n (%) | 2 (15.4) | 9 (69.2) | 7 (53.8) | 13 (100) |
| Right lower extremity, n (%) | 1 (7.7) | 8 (61.5) | 7 (53.8) | 13 (100) |
*Four patients (30.8%) were not assessed for UMN affecting the trunk
EMG, electromyography; IQR, interquartile range; LMN, lower motor neuron; SD, standard deviation; UMN, upper motor neuron