Table 1.
Functional class and hemodynamics before and after medical and surgical treatments
| WHO functional class |
PVRi (WU) |
CI (L/kg/m2) |
RVEF MRI (%) |
RVFAC ECHO (%) |
TAPSE ECHO (cm) |
RAP (mmHg) |
BNP (pg/ml) |
|
|---|---|---|---|---|---|---|---|---|
| At presentation | IV | 34.3 | 1.7 | 23 | 0.75 | 11 | 3120 | |
| 12 months of triple therapy | II | 12.2 | 3.6 | 39 | 1.75 | 7 | 13 | |
| Pre Potts shunt (18 months of triple therapy) | III | 22 | 3.3 | 49% | 35 | 1.75 | 4 | 19 |
| One year post Potts shunt | II | 26 | 3.4 | 47% | 34 | 1.8 | 3 | 15 |
Abbreviations: BNP, B‐type natriuretic peptide; CI, cardiac index; ECHO, echocardiography; PVRi, indexed pulmonary vascular resistance; RAP, right atrial pressure; RVEF, right ventricular ejection; RVFAC, right ventricular fractional area change; fraction; TAPSE, tricuspid annular plane systolic excursion.