Table 3.
Pulmonary function testing | • DLCO < 30% or worsening DLCO in the setting of preserved lung volumes |
6-Minute Walk Test | • Marked or worsening exertional desaturation • Severely reduced or worsening 6MWT distance • Impaired (decreased) heart rate recovery following exercise (< 13 beats per minute) |
CT scan | • Increased pulmonary artery to aorta ratio (> 0.9) • RV to LV ratio > 1 |
Echocardiogram | • RVSP elevation > 45 • RV dilation • TAPSE < 1.8cm • RVOT diameter > 3.4cm • Reduced RV fractional area change • Reduced RV ejection fraction on 3D ECHO |
Laboratory studies | • Elevated BNP |
ILD = interstitial lung disease. DLCO = diffusion capacity of carbon monoxide. 6MWT = 6-minute walk test. RV = right ventricle. LV = left ventricle. RVSP = right ventricular systolic pressure. TAPSE = tricuspid annular plane systolic exertion. RVOT = right ventricular outflow tract. ECHO = echocardiogram. BNP = brain natriuretic peptide. Adapted from King, et al. CHEST. 2020.245