Table I.
Clinical conditions associated with acquired haemophilia A (secondary forms)
Autoimmune disorders | Systemic lupus erythematosus, rheumatoid arthritis, temporal arteritis, multiple sclerosis, myasthenia gravis, ulcerative colitis, autoimmune haemolytic anaemia, Sjogren’s syndrome, Goodpasture’s syndrome, autoimmune thyroid diseases |
Malignancies | Haematological: chronic lymphocytic leukaemia, multiple myeloma, Waldenström’s macroglobulinaemia, monoclonal gammopathy of undetermined significance, non-Hodgkin’s lymphoma, myelodysplasia, myelofibrosis, other chronic myeloproliferative disorders Solid tumors: lung, prostate, pancreas, colon, stomach, melanoma, breast, kidney, head-neck |
Cutaneous diseases | Pemphigus, psoriasis |
Drugs | Chloramphenicol, sulphonamides, β-lactam antibiotics, phenytoin, methyldopa, non-steroidal anti-inflammatory drugs, Interferon-α, fludarabine, clopidrogrel. |
Pregnancy | Generally, 1–4 months after delivery or abortion, although also possible pre-partum |
Other disorders | Acute hepatitis B or C virus infection, chronic obstructive pulmonary disease, asthma |