TABLE 2.

Symptoms and abnormal results for all 39 study subjects

All subjects (n=39), 56.4% females, median age 13.5 years (range 2–18, interquartile range 8–15)			Functional or laboratory results in detail
Symptoms	Cough	19 (48.7%)
	Dyspnoea at rest	12 (30.8%)
	Exertional dyspnoea	30 (76.9%)
	Chest pain	7 (17.9%)
Abnormal functional or laboratory results	Spirometry	5 (13.2%)	1 with mild reduction and 1 with moderate reduction of vital capacity 2 with mild obstruction on F‐V loop, with positive BDT, and 1 with moderate obstruction on F‐V loop, with negative BDT
	6MWT	3 (8.8%)	Decline in oxygen saturation during 6MWT to 83%, 88% and 92% respectively
	DLCO	3 (11.5%)	Decline to 68%, 66% and 60% of predictive value, respectively
	Chest X‐ray	7 (18.9%)	2 with basal limited infiltration, 5 with perihilar opacities
	D‐dimers	2 (8%)	Girl with polymorphous symptoms without other abnormities and physiological result of repeated D‐dimers. Another girl (case 3 in Table 1).

Data presented as numbers (percentages). F‐V loop, flow‐volume loop, BDT, standardised bronchodilatation test with 4 puffs of salbutamol, 6MWT, 6‐minute walk test, DLCO, diffusing capacity for carbon monoxide.