Table 1.
N (%) or median (range) | |
---|---|
Age at onset, y | (2–91) |
Age at diagnosis, y | (2–91) |
Male | 89/160 (55.6) |
Chronic presentation (in >4 months) | 104/136 (76.5) |
Concomitant autoimmune diseases | 9/162 (5.6) |
History of cancer | 11/162 (6.8) |
Main complaints leading to consultation | |
Gait instability | 49/162 (30.2) |
Sleep disturbances | 48/162 (29.6) |
Movement disorders | 39/162 (24.1) |
Bulbar symptoms | 45/162 (27.8) |
Cognitive impairment | 17/162 (16.7) |
Other | 33/162 (20.4) |
Clinical phenotypes at diagnosis | |
Movement disorders | 61/162 (37.6) |
Bulbar syndrome | 37/162 (22.8) |
Cognitive disorder | 24/162 (14.8) |
Sleep disorder | 21/162 (13.0) |
Neuromusular | 9/162 (5.6) |
Unclassified | 10/162 (6.2) |
PSP-like | 22/162 (13.6) |