TABLE 3.

Metabolic profile and assay results.

	References range	Case 1	Case 2	Case 3	Case 4
Citrulline	10–60 mmol/L	27	16	13	32
Argininosuccinate	0–2 mmol/L	0	<2	<2	<2
Arginine	40–160 mmol/L	72	48	61	48
Ornithine	20–135 mmol/L	74	42	67	94
Aspartate	0–25 mmol/L	4	4	10	6
Glutamine	410–700 mmol/L	287	539	614	488
Urinary Orotic acid	0.2–1.5 mol/mol	Not tested	0.9	0.3	0.4
BAL or Blood PCR	NA	Neg	Neg	Neg	Neg
Mycoplasma Culture	NA	No sent	Neg	Neg	Neg
Ureaplasma Culture	NA	Not sent	Neg	neg	Neg
Specimen Type	NA	Not sent	Blood a	BAL Fluid b , (41,42)	Blood a

BAL, bronchoalveolar lavage, D, donor, NA, not applicable, Neg, Negative, PCR, polymerase chain reaction, R, recipient.

^aTest performed in ARUP laboratories.

^bTest performed in Mayo Clinic laboratories.