Table III.

Clinical studies on dental manifestations of vascular Ehlers-Danlos syndrome (vEDS)

Authors	Abnormalities in tooth number n (%)	Pulp shape modifications n (%)	Root fusion n (%)	Exceeding root length n (%)	Pulp calcification n (%)
De Coster et al., 2005 (41) (n = 6)	0	0	0	0	0
Ferre et al., 2012 (48) (n = 17)	0	12 (70.6)	8 (47.1)	11 (64.7)	0

Two case-control studies on 23 individuals with clinically and genetically diagnosed vEDS were published up to April 2019. None of the cases reported crown malformations or tooth discolorations. If not stated otherwise, number (n) and percentage (%) of affected individuals are given.