Table 2E.
IUIS classification of the patients with PID (2020) and JMF scores of the PID subgroups.
| Diagnoses | n | % | JMF scoreMean±SD | JMF scoreMedian (Min-Max) |
|---|---|---|---|---|
| Immunodeficiencies affecting cellular and humoral immunity | 18 | 18.4 | 3.28±1.60 | 3.00 (1-7) |
| Combined immunodeficiencies with associated syndromic features | 21 | 21.4 | 3.90±1.44 | 4.00 (1-6) |
| Immunodeficiencies due to Antibody Deficiencies | 39 | 39.8 | 2.95±1.58 | 2.00 (0-6) |
| Diseases of immune dysregulation | 7 | 7.1 | 2.14±1.57 | 2.00 (0-5) |
| Congenital defects of phagocyte number or function or both | 8 | 8.2 | 4.50±1.69 | 4.00 (2-7) |
| Defects in Intrinsic and Innate Immunity | 1 | 1 | 7.00±0.00 | 7.00 (7-7) |
| Auto-inflammatory disorders | 3 | 3.1 | 4.00±0.00 | 4.00 (4-4) |
| Complement deficiencies | 1 | 1 | 3.00±0.00 | 3.00 (3-3) |
| Bone marrow failure | 0 | 0.0 | . | . |
| Phenocopies of PID | 0 | 0.0 | . | . |
| Total | 98 | 100.0 |
IUIS, International Association of Immunology Societies.