Table 1.

Demographic characteristics and descriptive results.

Variable	Result
Gender	Female 57.5%, Male 42.5%
Mean age	53 years (SD = 17.9 years, 11–89 years)
Symptoms	No symptoms 32.3%, abdominal discomfort 48.8%, abdominal pain 40.3%, loss of weight 16.7%, fatigue 15.6%, jaundice 10.5%, fever 6.2%
WHO definition [13] *	possible 3.6%, probable 36.4%, confirmed 59.6%
PNM classification [14]	P: P0 0.4%, P1 2.9%, P2 33.1%, P3 20.1%, P4 42.7%, Px 0.8%
	N: N0 60.9%, N1 33.3%, Nx 5.8%
	M: M0 87.1%, M1 9.3%, Mx 3.6%
Disease stage [14]	stage I 2.8%, stage II 26.3%, stage IIIa 14.7%, stage IIIb 23.9%, stage IV 30.9%
Outcome	cured 14.4%, stable disease 62.2% (47.8% with BMZ, 14.4% without BMZ for M = 45.6 months, SD = 25.8), progressive disease 5.2%

* Possible case: any patient with clinical and epidemiological history and imaging findings or serology positive for AE. Probable case: any patient with clinical and epidemiological history, and imaging findings and serology positive for AE with two tests (indirect hemagglutinin, IgG EIA, Em2+ IgG, reEm18 IgG, and Echinococcus Western Blot IgG Essay). Confirmed case: (1) additional histopathology compatible with AE, and/or (2) detection of E. multilocularis nucleic acid sequence(s) in a clinical specimen.