Table 1.
Clinical and demographic characteristics of the population in the study.
| Variable | N (%) | Mean (SD) | Median (IQR) | Range |
|---|---|---|---|---|
| Age of symptoms onset (years) | 17 (100%) | 2.7 (3.1) | 1.5 (1.0–3.3) | 0.0–11.6 |
| Age at diagnosis (years) | 17 (100%) | 7.0 (4.2) | 6.6 (4.3–9.8) | 0.7–14.8 |
| Diagnosis delay (years) | 17 (100%) | 4.3 (3.8) | 3.2 (1.3–6.7) | 0.4–11.9 |
| Age at baseline HRCT (years) | 17 (100%) | 10.4 (3.0) | 10.7 (8.5–12.6) | 5.7–14.8 |
| Age at HRCT follow-up (years) | 13 (76%) | 14.7 (2.8) | 14.8 (13.7–16.5) | 9.1–18.1 |
| Duration of follow-up (years) | 17 (100%) | 3.4 (1.2) | 4.0 (3.2–4.0) | 0.4–4.9 |
| Pre-infusion IgG levels (mg/dl) | 12 (71%) | 910 (107) | 915 (872–964) | 716–1,080 |
IgG, immunoglobulin G; IQR, Interquartile range; SD, Standard deviation.