. Author manuscript; available in PMC: 2022 Jun 6.

Published in final edited form as: Hepatology. 2021 Mar;73(3):1088–1104. doi: 10.1002/hep.31421

TABLE 5.

Treatment Regimens Used for the Management of APAH in Our APECED Cohort at the Time of the NIH Evaluation

Treatment Regimen	Number of Patients (% of Total Patients with APAH)
Combination of prednisone with azathioprine	6 (33.3)
6-mercaptopurine or azathioprine monotherapy	4 (22.2)
Prednisone monotherapy	2 (11.1)
Combination of mycophenolate mofetil and rituximab	2 (11.1)
Cyclosporine monotherapy	1 (5.6)
Mycophenolate mofetil monotherapy	1 (5.6)
Combination of prednisone, mycophenolate mofetil, and tacrolimus^*	1 (5.6)
Combination of 6-mercaptopurine and cyclosporine^†	1 (5.6)

Combination immunosuppression was prescribed for limbal stem cell transplantation.

^†

Combination immunosuppression was prescribed because of initial difficulty to control APAH on 6-mercaptopurine monotherapy on prednisone weaning. Since then, the patient has been on azathioprine monotherapy with complete control of APAH.