Table 2.
Clinicopathological features of head and neck low-grade fibromyxoid sarcoma (n = 15)
| Case | Age (years)/Gender | Site | Size (cm) | Primary/Recurrent | MUC4 | FISH for FUS | Collagen rosettes | Original diagnosis+ or submitting pathologist’s diagnosis^ | Recurrence (Time to first recurrence in months) | Length of follow up (months) | Last known status |
|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 13/M | Cervico-dorsal | 5 | Recurrent | + | NP | + | Neurofibroma+ | + (72) | 156 | AWOD |
| 2 | 19/M | Nape of neck | 3.5 | Primary | + | NP | − | LGFMS+ | − | 66 | AWOD |
| 3 | 32/M | Supraclavicular | 4.6 | Primary | + | NP | − | LGFMS+ | − | 44 | AWOD |
| 4 | 15/F | Parapharyngeal | 6 | Primary | + | NP | − | LGFMS+ | − | 11 | AWOD |
| 5 | 22/F | Supraclavicular | NK | Primary | + | NP | − | LGFMS+ | − | 2 | AWOD |
| 6 | 34/F | Posterior neck | 6.3 | Recurrent | + | NP | − | Nodular fasciitis+ | + (60) | 216 | AWOD |
| 7 | 10/M | Orbit | 1.7 | Recurrent | + | NP | − | LGFMS^ | + (15) | 15 | AWOD |
| 8 | 17/F | Posterior neck | 3 | Primary | + | NP | − | LGFMS^ | − | 72 | AWOD |
| 9 | 58/F | Adjacent to thyroid gland | 2.7 | Primary | + | NP | − | Spindle cell neoplasm^ | NK | 0 | NK |
| 10 | 28/M | Neck (left) | 1.5 | Primary | + | + | − | None^ | − | 36 | AWOD |
| 11 | 28/F | Neck (right) | 1.5 | Primary | + | + | − | LGFMS^ | − | 36 | AWOD |
| 12 | 97/F | Supraclavicular | 0.7 | Primary | + | + | − | Solitary fibrous tumor, neural tumor, metastatic GIST; spindle cell carcinoma^ | − | 48 | AWD* |
| 13 | 26/F | Posterior neck | 7.1 | Primary | + | NP | + | Atypical spindle cell neoplasm^ | NK | 0 | NK |
| 14 | 3/M | Lower lip | 0.8 | Primary | + | + | − | LGFMS vs. clear cell sarcoma of soft tissue^ | NK | 0 | NK |
| 15 | 30/M | Supraclavicular | 3.1 | Primary | + | NP | + | Low-grade spindle cell neoplasm^ | NK | 0 | NK |
FISH fluorescence in situ hybridization; NP not performed; LGFMS low-grade fibromyxoid sarcoma; GIST gastrointestinal stromal tumor; Y Yes; N No; NK not known; N/A not applicable; R recurrence; AWOD Alive without disease; AWD Alive with disease
*Patient was treated with local radiation only