Table 1.
Subject characteristics
| All four experiments | No OPTT or MMTT | |
|---|---|---|
| n | 3 female, 5 male | 3 female, 5 male |
| Age at enrollment, median (range) | 8.5 years (3–15 years) | 2.5 years (10 months–7 years) |
| Genotype/phenotype | ||
| ABCC8, dominant diazoxide responsive | 4 | 1 |
| ABCC8, dominant diazoxide unresponsive | 2 | 0 |
| ABCC8, biallelic recessive diazoxide unresponsive | 2 | 4 |
| ABCC8, monoallelic recessive diazoxide unresponsive | 0 | 1 |
| KCNJ11, dominant diazoxide responsive | 0 | 1 |
| Unknown, partially diazoxide responsive | 0 | 1 |
| Pancreatectomy | ||
| No | 5 | 3 |
| 55% resection | 0 | 1 |
| 98% resection | 3 | 4 |
| HI management at enrollment | ||
| Diazoxide | 4 | 1 |
| Octreotide | 1 | 0 |
| Enteral 20% dextrose | 0 | 2 |
| Diazoxide + enteral 20% dextrose | 0 | 2 |
| Octreotide + enteral 20% dextrose | 1 | 2 |
| None | 2 | 1 |
Data are n unless otherwise indicated.