Table 1.

Baseline patient characteristics

Characteristic	Patients (N = 33)
Gender (male), n (%)	26 (78.8)
Age (years), mean(SD)	60.5 (13.2)
Diagnosis, n (%)
ALS	25 (75.8)
PMA	5 (15.2)
PLS	3 (9.1)
Site of onset, n (%)
Bulbar	7 (21.2)
Spinal	26 (78.8)
Nightly NIV, n (%)	3 (12.1)
Gastrostomy, n (%)	2 (6.1)
Telehealth use, n (%)	29 (87.8)
Respiratory function (% of predicted VC), mean (SD)	78.4 (25.6)
Disease duration from first symptoms (months), median (IQR)	35.6 (17.2–52.2)
ALSFRS-R, mean (SD)	35.9 (7.3)
ALSFRS-R (respiratory domain), mean (SD)	11.0 (1.3)

ALS amyotrophic lateral sclerosis, PMA progressive muscular atrophy, PLS primary lateral sclerosis, NIV non-invasive ventilation, VC vital capacity, SD standard deviation, IQR interquartile range, MND motor neuron disease, ALSFRS-R revised ALS functional rating scale