Table 1.
The frequencies of common allergic diseases among the studied IEI groups.
| Predominately antibody deficiency IUIS # III Median% (IQR). 40.3 (19.2–62.5) |
Combined immunodeficiencies IUIS #I&II Median% (IQR). 20 (10–32) |
Congenital phagocytic defects IUIS #V Median% (IQR). 10 (5–15.5) |
Immune dysregulation IUIS # IV Median% (IQR). 6 (1–10) |
Auto inflammatory IUIS # VII Median% (IQR). 2 (0–5) |
Test value• | P-value | |
|---|---|---|---|---|---|---|---|
| A. Food allergy Median (IQR) |
0.0 (0.0–5.0) | 0.8 (0.0–8.0) | 0.0 (0.0–0.0) | 0.0 (0.0–10.0) | 0.0 (0.0–0.0) | 10.598 | 0.031 |
| B. Allergic rhinitis Median (IQR) |
17.95 (5.0–40.0) | 5.0 (0.0–20,0) | 0.0 (0.0–11.3) | 0.0 (0.0–15.0) | 0.0 (0.0–0.0) | 27.854 | <0.001 |
| C. Bronchial asthma Median (IQR) |
36.0 (10.7–50.0) | 13.5 (0.0–20.0) | 0.0 (0.0–10.0) | 0.0 (0.0–17.5) | 0.0 (0.0–0.0) | 34.229 | <0.001 |
| D. Atopic dermatitis Median (IQR) |
8.0 (1.0–20.0) | 30.0 (10.0–60.0) | 0.0 (.00–11.1) | 9.5 (0.0–50.0) | – | 16.517 | 0.001 |
|
Post hoc analysis∗ |
||||||||||
|---|---|---|---|---|---|---|---|---|---|---|
| Parameters | P1 | P2 | P3 | P4 | P5 | P6 | P7 | P8 | P9 | P10 |
| A. Food allergy | 0.683 | 0.077 | 0.577 | 0.027 | 0.042 | 0.869 | 0.014 | 0.055 | 0.597 | 0.019 |
| B. Allergic rhinitis | 0.014 | 0.001 | 0.003 | <0.001 | 0.230 | 0.555 | 0.002 | 0.637 | 0.061 | 0.014 |
| C. Bronchial asthma | 0.015 | <0.001 | <0.001 | <0.001 | 0.019 | 0.126 | <0.001 | 0.368 | 0.212 | 0.033 |
| D. Atopic dermatitis | 0.007 | 0.032 | 0.799 | – | <0.001 | 0.108 | – | 0.038 | – | – |
∗ Kruskall-Wallis test followed by post hoc analysis. P values are significant if < 0.05.
P1: Predominantly antibody deficiency vs combined immunodeficienicies.
P2: Predominantly antibody deficiency vs congenital defects of phagocytosis.
P3: Predominantly antibody deficiency vs immune dysregulation.
P4: Predominantly antibody deficiency vs autoinflammatory disorders.
P5: Combined immunodeficienicies vs congenital defects of phagocytosis.
P6: Combined immunodeficienicies vs immune dysregulation disorders.
P7: Combined immunodeficienicies vs autoinflammatory disorders.
P8: Congenital defects of phagocytosis vs immune dysregulation disorders.
P9: Congenital defects of phagocytosis vs auto inflammatory disorders.
P10: Iimmune dysregulation vs auto inflammatory disorders