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. Author manuscript; available in PMC: 2023 Jul 1.
Published in final edited form as: Heart Fail Clin. 2022 Jul;18(3):479–488. doi: 10.1016/j.hfc.2022.02.005

Table 2.

Staging systems cardiac amyloidosis

AL Points Stage Median Survival, mo.
0 I >120
1 II 69
2 III 16
3 IV 6
ATTR 0 I 69.2
1 II 46.7
2 III 24.1

AL 1 point each for dFLC >180mg/L; NTproBNP >1800 pg./mL; HS TroponinT ≥40ng/L(61)

ATTR 1 point each for NTproBNP>300ng/L; eGFR<45 mL/min(62)