| AIP |
Acute intermittent porphyria |
| AHP |
Acute Hepatic Porphyrias |
| ALA |
-aminolevulinic acid |
| ALAS1 |
ALA synthase 1 |
| APA |
acute porphyric attack |
| AP-AC |
AHP patient—asymptomatic carrier |
| AP-BA |
AHP patient—asymptomatic with biochemical alterations |
| AP-SP |
AHP patient—symptomatic |
| ED |
endothelial dysfunction |
| ET1 |
serum endothelin-1 |
| HMBS |
hydroxymethylbilane synthase |
| IV |
intravenous |
| IU |
International Units |
| NO |
nitric oxide |
| NOS |
NO synthase |
| PAKD |
porphyria-associated kidney disease |
| PBG |
porphobilinogen |
| PPOX |
protoporphyrinogen oxidase |
| PRES |
posterior reversible encephalopathy syndrome |
| sGC |
soluble guanylate cyclase |
| ULN |
upper level of normal |
| VP |
Variegate Porphyria |