TABLE 2.
The immune associate results of reported X-MAID patients and our case.
| P1 | P2 | P3 | P4 | P5 | P6 | P7 | P8 | P9 | P10 | P11 | P12 | This case | |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Neutrocytes | L | L | L | L | L | L | N | L | L | N | L | L | L |
| Monocytes | L | L | L | N | L | L | L | L | L | N | ND | ND | L |
| Lymphocytes | L | L | L | L | L | L | L | L | L | L | L | L | N |
| CD19+ cells | L | L | L | L | L | L | L | L | L | L | L | L | L |
| Naive B cells | L | L | L | ND | ND | ND | ND | ND | N | ND | ND | ND | L |
| Natural killer cells | L | L | L | L | L | L | L | ND | ND | L | N | L | L |
| CD4+ cells | L | L | L | L | L | L | L | L | L | L | L | L | L |
| CD8+cells | L | L | L | L | L | N | L | L | L | L | L | L | L |
| Naive CD4+T cells | L | L | L | ND | L | L | L | N | L | ND | ND | ND | N |
| Naive CD8+T cells | L | L | L | ND | L | L | L | L | N | ND | ND | ND | N |
| CD57+CD8+ T cells | H | H | H | ND | H | H | H | ND | ND | ND | ND | ND | N |
| IgG | L | L | L | L | NE | L | L | L | L | N | ND | ND | N |
| IgA | L | N | L | L | L | L | N | N | L | L | ND | ND | N |
| IgM | L | L | L | L | L | L | L | L | L | L | ND | ND | N |
| IgE | NE | N | NE | N | N | NE | NE | N | N | ND | ND | ND | N |
L, low; H, high; N, normal; NE, Non-evaluated; ND, not determined; Ig, immunoglobin.