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. 2022 Jun 22;44(1):1061–1069. doi: 10.1080/0886022X.2022.2089167

Table 1.

Clinical features of 8 children with anti-CFH Ab-associated HUS.

  Case 1 Case 2 Case 3 Case 4 Case 5 Case 6 Case 7 Case 8
Age (years) 5.83 7 7.33 6.33 9.59 13.5 5.92 6.33
Sex Male Male Male Male Female Male Female Female
Prodrome Vomiting Vomiting, abdominal pain, fever, cough Vomiting, fever, cough Vomiting, abdominal pain, diarrhea Vomiting, cough Cough None Vomiting, abdominal pain, fever, cough
Time of onset November May December November May November June November
Jaundice Yes Yes Yes Yes Yes Yes Yes No
Petechia Yes Yes Yes Yes Yes Yes Yes No
Hypertension No No No Yes No No No Yes
Oliguria/Anuria Yes Yes No Yes No Yes Yes Yes
Edema Yes Yes Yes Yes Yes Yes Yes Yes
Hematuria Yes Yes Yes Yes Yes Yes Yes Yes
Proteinuria Yes Yes Yes Yes Yes Yes Yes Yes
Hepatic involvement No Yes Yes Yes No Yes Yes No
Other extrarenal involvement Pulmonary hemorrhage, gastrointestinal hemorrhage, multiple organ failure no Epistaxis, gastrointestinal hemorrhage Pancreatitis No No No Convulsions, hypertensive encephalopathy, severe pneumonia, respiratory failure