Table 1.
Clinical features of 8 children with anti-CFH Ab-associated HUS.
Case 1 | Case 2 | Case 3 | Case 4 | Case 5 | Case 6 | Case 7 | Case 8 | |
---|---|---|---|---|---|---|---|---|
Age (years) | 5.83 | 7 | 7.33 | 6.33 | 9.59 | 13.5 | 5.92 | 6.33 |
Sex | Male | Male | Male | Male | Female | Male | Female | Female |
Prodrome | Vomiting | Vomiting, abdominal pain, fever, cough | Vomiting, fever, cough | Vomiting, abdominal pain, diarrhea | Vomiting, cough | Cough | None | Vomiting, abdominal pain, fever, cough |
Time of onset | November | May | December | November | May | November | June | November |
Jaundice | Yes | Yes | Yes | Yes | Yes | Yes | Yes | No |
Petechia | Yes | Yes | Yes | Yes | Yes | Yes | Yes | No |
Hypertension | No | No | No | Yes | No | No | No | Yes |
Oliguria/Anuria | Yes | Yes | No | Yes | No | Yes | Yes | Yes |
Edema | Yes | Yes | Yes | Yes | Yes | Yes | Yes | Yes |
Hematuria | Yes | Yes | Yes | Yes | Yes | Yes | Yes | Yes |
Proteinuria | Yes | Yes | Yes | Yes | Yes | Yes | Yes | Yes |
Hepatic involvement | No | Yes | Yes | Yes | No | Yes | Yes | No |
Other extrarenal involvement | Pulmonary hemorrhage, gastrointestinal hemorrhage, multiple organ failure | no | Epistaxis, gastrointestinal hemorrhage | Pancreatitis | No | No | No | Convulsions, hypertensive encephalopathy, severe pneumonia, respiratory failure |