Table 1.
References | Sex/age (years) | Onset | Main manifestations | MRI findings | Treatment | Outcome |
---|---|---|---|---|---|---|
Zuliani et al. (1) | F/65 | Subacute | CA, vertigo, vomiting | Normal | Steroids | No benefit |
Höftberger et al. (6) | M/38 | Acute | CA, encephalitis, seizures, papilledema vomiting | Cerebellar atrophy (f-u) | Steroids, IVIg | Partial recovery |
Xu et al. (7) | F/51 | Insidious | CA, dizziness, RBD | Cerebellar atrophy (f-u) Hot cross Bun sign | Steroids, MMF | Partial recovery |
Liu et al. (8) | F/46 | Insidious | CA | Cerebellar atrophy (f-u) | Steroids, MMF | Partial recovery |
M/14 | Subacute | CA, encephalitis, myeloradiculopathy | Diffuse cerebellar T2W hyperintensities | Steroids, IVIg | Partial recovery with relapses | |
M/65 | Insidious | CA, RBD | Cerebellar and pons atrophy (f-u) Hot cross Bun sign | Steroids, IVIg, PE | No benefit with deterioration | |
F/84 | Subacute | CA | Normal | Steroids | Stability | |
F/69 | Subacute | CA, encephalopathy, radiculoneuropathy | Diffuse cerebral (FLAIR) hyperintensities | IVIg, steroids | Partial recovery with relapses | |
This report | M/10 | Acute | CA, encephalopathy | Diffuse cerebellar T2W hyperintensities; cerebellar atrophy (f-u) | Steroids, IVIg | Almost complete recovery |
CA, cerebellar ataxia; F-u, follow-up; MMF, mycophenolate mofetil; RBD, REM-sleep behavior disorder.