TABLE 1.

The diagnosis of Marfan syndrome (M) relies on defined clinical criteria (Ghent nosology).

Patients	With or without family history	With or without EL	Ao (Z-score)	Systemic score
M1	With	With	5	7
M2	With	With	4	9
M2	With	With	3	8

Ao, aortic diameter at the sinuses of Valsalva above indicated Z-score or aortic root dissection; EL, ectopia lentis.