Table 1:
Patient characteristics
| Male/female, n | 24/26 |
|---|---|
| Primary diagnosis, n (%) | |
| TA | 12 (24) |
| HLHS | 10 (20) |
| DILV + TGA | 10 (20) |
| DORV | 6 (12) |
| uAVSD | 4 (8) |
| ccTGA | 4 (8) |
| PA + IVS | 2 (4) |
| Others | 2 (4) |
| Dominant ventricle | |
| Left, n (%) | 29 (58) |
| Right, n (%) | 16 (32) |
| Biventricular/indeterminate, n (%) | 5 (10) |
| Characteristics at Fontan procedure | |
| Age at Fontan, years | 3.7 (1.9) |
| Implanted conduit size (16/18/20 mm), n | 26/18/6 |
| Height, cm | 99 (11) |
| Weight, kg | 15.0 (2.9) |
| BSA, m2 | 0.64 (0.09) |
| Characteristics at time of MRI | |
| Age at MRI, years | 16.9 (4.5) |
| Height, cm | 167 (11) |
| Weight, kg | 57 (14) |
| BSA, m2 | 1.62 (0.24) |
| Time between Fontan and MRI, years | 13.2 (4.1) |
| NYHA class I–II, n (%) | 50 (100) |
| CPET | |
| Peak VO2 (n = 44), ml/kg/min | 26.4 (5.6) |
Values are reported as mean (SD) unless otherwise specified.
(cc)TGA: (congenital corrected) transposition of the great arteries; BSA: body surface area; CPET: cardiopulmonary exercise testing; DILV: double inlet left ventricle; DORV: double outlet right ventricle; HLHS: hypoplastic left heart syndrome; MRI: magnetic resonance imaging; NYHA: New York Heart Association; PA + IVS: pulmonary atresia with intact ventricular septum; SD: standard deviation; TA: tricuspid atresia; uAVSD: unbalanced atrioventricular septal defect.