Table 1.
N = 32 (%) | |
---|---|
Gender, no (%) | |
Female | 2 (6.2%) |
Male | 30 (93.8%) |
PID subtype, no (%): | |
CID | 17 (53.1%) |
PIRD | 6 (18.8%) |
CGD | 9 (28.1%) |
Age (years) of first symptoms (median, range) | 1.70 [0.06;34.3] |
Age (years) at clinical diagnosis (median, range) | 3.81 [0.27;34.8] |
Time between first symptoms and diagnosis (median, range) | 0.41 [0.00;14.2] |
Age at transplant (median, range) | 26.9 [17.2;41.4] |
Delay between diagnosis and allo-HSCT (median, range) | 19.4 [2.03;38.3] |
Active infection at time of allo-HSCT | 16 (50.0%) |
History of AI | 20 (62.5%) |
Active AI at time of allo-HSCT, no (%) | 13/20 (65.0%) |
History of lymphoma, no (%) | 9 (28.1%) |
Preallo-HSCT chemotherapy, no (%) | 9 (28.1%) |
IgRT prior to allo-HSCT, no (%) | 9 (59.4%) |
Splenectomy, no (%) | 7 (21.9%) |
Age at splenectomy (median, range) | 8.00 [3.00;36.0] |
HTC-CI score, no (%) | |
High (>2) | 16 (50%) |
Intermediate (1–2) | 13 (40.6%) |
Low (0) | 3 (9.38%) |
Main organ contributing to HCT-CI score (%) | |
Pulmonary | 16 (50%) |
Hepatitis | 4 (12.5%) |
Active IBD | 4 (12.5%) |
AI autoimmunity/autoinflammation (AI), HCT-CI hematopoietic cell transplantation-comorbidity index.