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. 2021 Aug 3;36(8):1694–1701. doi: 10.1038/s41433-021-01711-x

Table 2.

List of PAX6 mutations causing cataract including spectrum of other eye anomalies.

S.no Origin HGVSc HGVSp Phenotype Reference
1. America

c.388 C>T

c.1058 C>G

p.Arg130*,

p.Ser353* compound heterozygous

Aniridia, nystagmus, foveal hypoplasia, congenital lamellar cataract, late onset corneal dystrophy Glaser et al. 1994
2. France c.137 T>C p. Leu46Pro Bilateral microphthalmia, nystagmus and cataract Dansault et al. 2007
3. France c.143delG P. Val48fsX53 bilateral aniridia associated with congenital cataract, foveal hypolasia, and nystagmus Dansault et al. 2007
4. America c.112 C>T p.Arg38Trp Microcornea, cataract Solomon et al. 2009
5. France c.718 C>T p.Arg240*Ter Aniridia, congenital cataract Brémond-Gignac et al. 2010
6. China c.113_129del17 p.Arg38ProfsX12 Aniridia, congenital cataract Cai F et al. 2010
7. UK c.227 C>G p.Pro76Arg Nystagmus, foveal hypoplasia and presenile cataract Thomas et al. 2014
8. South Africa c.622 G>A p.Arg208Thr Coloboma, nystagmus, variable cataract Goolam et al. 2018
9. UK c.184 G>A p.Val62Met Congenital cataract, congenital nystagmus Present study 2021

* designated to truncated protein.