| Metabolites | |
| 5-ALA | 5-aminolevulinic acid/aminolevulinate |
| COPRO | coproporphyrin |
| URO | uroporphyrin |
| PBG | porphobilinogen |
| HMB | 1-hydroxymethylbilane/pre-uroporphyrinogen |
| UROgen | uroporphyrinogen |
| COPROgen | coproporphyrinogen |
| PROTOgen | protoporphyrinogen |
| PpIX | protoporphyrin IX |
| Organelles | |
| PM | plasma membrane |
| ER | endoplasmic reticulum |
| GA | Golgi apparatus |
| OMM/IMM | outer/inner mitochondrial membrane |
| IMS | inner mitochondrial space |
| END | endosome |
| LYSO | lysosome |
| Enzymes | |
| ALAS | ALA-synthase |
| PLP | pyridoxal-5’-phosphate |
| ALAD | ALA-dehydratase |
| PBGD | porphobilinogen deaminase |
| UROS | uroporphyrinogen III cosynthase |
| UROD | uroporphyrinogen decarboxylase |
| CPO | coproporphyrinogen III oxidase |
| PPO | protoporphyrinogen oxidase |
| FECH | ferrochelatase |
| HO | heme oxygenase |
| BVRA | biliverdin reductase-A |
| UGT1A1 | UDP-glucuronosyltransferase 1A1 |
| Others | |
| PDT | photodynamic therapy |
| PDD | photodynamic diagnosis |
| ROS | reactive oxygen species |
| TCA | tricarboxylic acid |
| CLIP | cytosolic labile iron pool |
| ISC | iron-sulfur cluster |
| CO | carbon monoxide |
| ABCB | ATP-binding cassette subfamily B member |