Table 4.

Baseline Characteristics.

Characteristic		Pt.1		Pt.2		Pt.3		Pt.4		Pt.5
Age		56		29		44		57		35
Sex		F		F		M		F		F
Disease onset		HF		HF		HF		HF		VT
Family history
DCM		+		+		+		+		-
SCD <45y		-		-		+		-		-
Symptoms
Syncope		-		-		-		-		+
NYHA		II		III		III		II		I
ECG abnormalities
Low voltage		-		-		-		+		+
Reduced R amplitude		-		+		+		+		+
Repolarization abnormalities		+		-		-		-		-
TTE
LVDd/LVDs (mm)		53/44		68/59		74/71		54/48		46/43
IVS/PW (mm)		9/6		9/7		10/10		8/8		8/6
LVEF (%)		35		35		9		24		30

‘Low voltage’ is defined as QRS peak-to-peak amplitude in leads I, II, and III <0.5 mV, the sum of the amplitudes <1.5 mV, and amplitude in all precordial leads <1.0 mV (3). ‘Reduced R amplitude’ is defined as R waves <3 mm for at least five of six limb leads or <5 mm for five of six precordial leads (8). ‘Repolarization abnormalities’ is defined as fulfilling the major or minor criteria as described in the modified ARVC/D task force criteria (18).

ARVC/D: arrhythmogenic right ventricular cardiomyopathy/dysplasia, DCM: dilated cardiomyopathy, ECG: electrocardiogram, IVS: interventricular septum, LVDd: left ventricular end-diastolic dimension, LVDs: end-systolic dimension, LVEF: left ventricular ejection fraction, PW: posterior wall, SCD: sudden cardiac death, TTE, transthoracic echocardiography