Table 4.
First author | Reason for exclusion | Study design | Period of data collection | Country (Place) | Number of cases | Demographics of study participants | PPGL incidence per 100,000/ annum | PGL incidence per 100,000/ annum | PCC incidence per 100,000/ annum | ||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
PCC | PGL | Total | M (n) | F (n) | Age range | Median age | Mean age | ||||||||
Dua [26] | Carotid body PGLs only | Retrospective (nationwide) | 1998-2011 | US | 684 | 684 | 271 | 413 | 53.8 | 1998 0.07 2011 0.1 |
- | ||||
Ebbehoj [27] | PCCs only | Retrospective (multicentre) | 1995-2017 | Olmsted County, MN, USA | 14 | - | 14 | 5 | 9 | 26-70 | 46 | - | 0.4 | ||
Takayanagi [28] | Survey | Nationwide | 1997 | Japan | 1030a | NR | 1030a | - | - | - |
Abbreviations: M, male; F, female; PCC, pheochromocytoma; PGL, paraganglioma; PPGL, pheochromocytoma and paraganglioma.
aEstimated number.