Table 2.
Morphometric characterization and other mechanisms of hindbrain ptosis in CM-I type A, and the corresponding surgical intervention.
| Instability of CCJ | Tethering | Hydrocephalus | Intracranial Mass | Pressure Dissociation | |
|---|---|---|---|---|---|
| VPCF | normal | normal | normal | normal | normal |
| VAFM | normal | normal | normal | normal | normal |
| VBPCV/VPCF | normal | normal | normal/large | normal/large | normal |
| Brainstem and Cerebellum | normal | elongation and downward displacement | normal | normal | |
| Cause | cranial settling | traction | pressure coning | Hypotension of intraspinal canal | |
| Intervention | CCF | untethering/SFT | VPS | resection of mass or FMD | others |
Abbreviations: CM-I: Chiari malformation, CCJ = craniocervical junction, VPCV: volume of the posterior cranial fossa, VAFM: volume of area of surrounding foramen magnum, PFBV: volume of brain in posterior cranial fossa, CCF: craniocervical fixation, SFT: section of filum terminale, VPS: ventriculo-peritoneal shunt.