Table 1.

Table of Abbreviations.

ADAMTS13	a disintegrin and metalloproteinase with a thrombospondin type 1 motif, member 13
aHUS	atypical hemolytic uremic syndrome
AP	alternative pathway
APAS	antiphospholipid antibody syndrome
aPL	anionic phospholipid (e.g., phosphatidyl serine)
AT	anti-thrombin
BK	bradykinin
C1-INH	C1 inhibitor
C3aR, C5aR, C5aL2	receptors for C3a and C5a
CP	classical pathway
CPB2	carboxypeptidase B2
CS	contact system
CsA	chondroitin sulfate A
DAMP	damage/danger associated molecular pattern
FB	factor B
FD	factor D
FH	factor H
HITT	heparin induced thrombocytopenia and thrombosis
HK	high molecular weight kininogen
LP	lectin pathway
MAC	membrane attack complex (C5b-9)
MASP	MBL-associated serine protease
MBL	mannose binding lectin
MMP	matrix metalloprotease
NETs	neutrophil extracellular traps
PAI-1	plasminogen activator inhibitor-1
PAMP	pathogen associated molecular pattern
PAR	protease activated receptor
PC, APC	protein C, activated PC
PF4	platelet factor 4
Pg	plasminogen
PGI	prostacyclin
PK, PKa	plasma prekallikrein, plasma kallikrein
PNH	paroxysmal nocturnal hemoglobinuria
PRM	pathogen recognition molecule
prothrombinase	Factor Va/Factor Xa (FVa/FXa) enzymatic complex
PSGL-1	P-selectin glycoprotein 1
SUSD4	sushi domain-containing protein 4
TAFI	thrombin activatable fibrinolysis inhibitor, activated TAFI
tenase	TF/Factor VIIa (TF/FVIIa) enzymatic complex
TF	tissue factor
TFPI	tissue factor pathway inhibitor
tPA	tissue type plasminogen activator
ULIC	ultra large immune complexes
VWF, ULVWF	von Willebrand Factor, ultra large multimeric VWF