Figure 2.
Cardiac visualization of proband. (A–C)—ultrasound cardiography. (C–E)—cardiac MRI with gadolinium. (A)—enlarged right ventricle and normal size of left ventricle; (B)—sever tricuspid regurgitation (Doppler). (C)—left ventricular noncompaction, ratio of noncompact and compact layers 3.5: 1, (D,E)—foci of late gadolinium enhancement in septum (subendocardial, intramyocardial), right ventricle and anterior wall of left ventricle (subepicardial).
