Table 1.
Presentation | Arrhythmias | Valvular disease | CMR findings | Management | |
---|---|---|---|---|---|
Patient 1 | Sudden cardiac arrest | VF arrest | Bileaflet MVP, moderate MR | Diffuse myocardial fibrosis, LGE inferolateral wall | ICD placement |
Patient 2 | Syncope | Inducible VT on EP study | Bileaflet MVP, moderate MR | LGE inferior and inferolateral | ICD placement |
Patient 3 | Follow-up known valvular disease | 14.5% VE burden on cardiac event monitor | Myxomatous MV disease, severe MR | Reduced LVEF, diffuse myocardial fibrosis, LGE mid-inferior wall | Percutaneous mitral valve repair with significant decrease in VE burden |
Patient 4 | Follow-up known valvular disease | Rare VE | Bileaflet MVP, mild-moderate MR | Not performed | Medical management |
Patient 5 | Follow-up known valvular disease | 8.1% VE burden and non-sustained VT on cardiac event monitor | Bileaflet MVP, moderate MR | Myocardial fibrosis, no LGE | Referred for EP consult, medical management |
EP, electrophysiology; LGE, late gadolinium enhancement; LVEF, left ventricular ejection fraction; MR, mitral regurgitation; MVP, mitral valve prolapse; VE, ventricular ectopy; VF, ventricular fibrillation; VT, ventricular tachycardia.