Fig. 2.

Vitamin D levels in genetic subtypes of ichthyosis. Keratinopathic ichthyosis (KPI), Harlequin ichthyosis (HI), lamellar ichthyosis (LI), Netherton syndrome (NTS) and other syndromic ichthyoses show lowest vitamin D values, patients with milder types of ichthyosis (ichthyosis vulgaris (IV), X-linked ichthyosis (XLI)) only have a moderate insufficiency. Reference value for vitamin D sufficiency ≥30 ng/ml. CIE: congenital ichthyosiform erythroderma; HI: Harlequin ichthyosis; ARCI: autosomal recessive congenital ichthyosis.